l carnitine mitochondrial disease Role of in | Nutrition & Metabolism Carnitines as Mitochondrial Modulators of

These interactions modulate GS activity, influencing cellular processes such as nitrogen assimilation, carbon metabolism, and stress responses

[DOI] [PubMed] [Google Scholar] 233.Gabarin N, Gavish H, Muhlrad A, Chen YC, Namdar-Attar M, Nissenson RA, et al

Acknowledgements This research was supported in part by the Intramural Research Program of the National Institutes of Health, National Cancer Institute and National Institute of Arthritis and Musculoskeletal and Skin Diseases

The synthesis of glutathione is a tightly regulated process dependent on the availability of cysteine, which is both a substrate and a regulator at different synthesis stages